* It is persistence of the primary vitreous and hyaloid arterial system.
* Almost always unilateral (~90%)
*It is associated with Patau syndrome (Trisomy 13) .
* Presents as white pupillary reflex in the newborn (congenital leukocoria)
*It is usually associated with cataract, glaucoma , long and extended ciliary processes because of pull from contracted retrolental tissue, micropthalmos, intraocular hemorrhage and tractional retinal detachment.
* Investigations : USG and CT scan
* Differential diagnosis with retinoblastoma is done on the basis of micropthalmos and elongated ciliary processes.
* If diagnosed early, treatment is aspiration of lens, excision of retrolental membrane and vitrectomy.
* Visual prognosis is poor.
No comments:
Post a Comment